Megacystis Megacolon Intestinal Hypoperistalsis Syndrome: A Rare Entity!
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چکیده
منابع مشابه
Megacystis Megacolon Intestinal Hypoperistalsis Syndrome: A Rare Entity!
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is now a well established entity [1,2]. Also known as Berdon syndrome [1], it is characterized by massive abdominal distension caused by a largely dilated non obstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis. Isolated cases of congenital megacystis [3,4] and microcolon without megacystis [5] h...
متن کاملMegacystis-Microcolon-Intestinal Hypoperistalsis Syndrome
We report a case of megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS) in a newborn female infant who presented with an abdominal mass, absent bowel sounds, and feeding intolerance with bilious emesis. MMIHS is a rare congenital bowel and bladder defect requiring surgery and chronic total parenteral nutrition in an attempt to sustain life. With few exceptions, it is predominately...
متن کاملMegacystis microcolon intestinal hypoperistalsis syndrome.
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is a rare and the most severe form of functional intestinal obstruction in the newborn. The major features of this congenital and usually lethal anomaly are abdominal distension, bile-stained vomiting, and absent or decreased bowel peristalsis. Abdominal distension is a consequence of the distended, unobstructed urinary bladder w...
متن کاملMegacystis-Microcolon-Intestinal Hypoperistalsis Syndrome (MMIHS).
Introduction Megacystismicrocolon -intestinal hypoperistalsis syndrome(MMIHS) also called as BERDON SYNDROME is a rare congenital disease characterized by massive abdominal distension caused by a largely dilated non-obstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis. It poses a diagnostic and therapeutic challenge to the surgeon. It the most severe form of fun...
متن کاملMEGACYSTIS-MICROCOLON-INTESTINAL HYPOPERISTALSIS SYNDROME - report of a very rare pathology in a neonate
We are reporting a baby who presented with features of neonatal intestinal obstruction, with an x-ray picture suggestive of hold up at the duodenal level. On laparotomy he had malrotation of the gut which was corrected. He also had a dilated urinary bladder, which later on was treated with vasicostomy. The baby did not move his bowel inspite of no mechanical obstruction and even bypass procedur...
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ژورنال
عنوان ژورنال: Journal of Pediatrics & Neonatal Care
سال: 2017
ISSN: 2373-4426
DOI: 10.15406/jpnc.2017.07.00297